Surgical Management of Hand Deformity in Epidermolysis Bullosa
نویسندگان
چکیده
منابع مشابه
The surgical management of dystrophic epidermolysis bullosa (excluding the hand).
Fifty patients with Dystrophic Epidermolysis Bullosa (DEB) underwent surgery including release of limb, oral, anal, eye and penile contractures and treatment of chronic skin ulceration or skin tumours. Correction of contractures involves extensive release of skin and underlying tissues, with split skin grafting of secondary defects. Specific regions are discussed. Recurrence is inevitable due t...
متن کاملLimited Hand Surgery in Epidermolysis Bullosa
Epidermolysis bullosa (EB) is the name given to a group of rare congenital diseases with similar clinical symptoms. Their common feature is the susceptibility of the epithelia and skin to injury. Even minor shear forces from the sideways stretching of the skin contribute to epidermal tearing with blister formation. These blisters turn into wounds. In the most severe forms of the disease, wounds...
متن کاملSurgical management of epidermolysis bullosa: Proceedings of the IInd International Symposium on Epidermolysis Bullosa, Santiago, Chile, 2005.
From the Division of General and Thoracic Pediatric Surgery, Division of Pediatric Dermatology, and the Epidermolysis Bullosa Center, Cincinnati Children’s Hospital Medical Center, Cincinnati, Ohio, Great Ormond Street Hospital for Children, London, UK, St John’s Institute of Dermatology, Guy’s and St Thomas’ NHS Foundation Trust, London, UK, Departments of Hand Surgery and Dentistry, Clínica A...
متن کاملSuprathel(®) -assisted surgical treatment of the hand in a dystrophic epidermolysis bullosa patient.
Epidermolysis bullosa (EB) is a progressive familial disorder composed of dermal mucosal blisters, flexion contractures and pseudosyndactylies. Flexion contractures and pseudosyndactyly can be treated with surgery but usually require skin grafting. Because of poor wound healing, skin graft harvesting is a challenge in these patients. In order to prevent donor-site morbidities due to skin graft ...
متن کاملDental management of patients with epidermolysis bullosa.
Epidermolysis Bullosa (EB) is a group of rare, genetic skin disorders characterized by fragility and blistering to minimal trauma. All oral surfaces may be involved, including the tongue, buccal mucosa, palate, floor of the mouth and gingiva. Common oral findings of the disease include microstomia, intraoral ulcerations and bullae formation, ankyloglossia, tongue atrophy, elimination of buccal ...
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ژورنال
عنوان ژورنال: Plastic and Reconstructive Surgery - Global Open
سال: 2020
ISSN: 2169-7574
DOI: 10.1097/gox.0000000000002666